Question 1

Which ethnic group has the greatest number of people with cystic fibrosis?

Accepted Answer

A)   African Americans
B)  Asians
C)  Hispanics
D)  whitesE) A) and C)
F) None of the above

Question 2

Your patient has a lung infection with Pseudomonas aeruginosa. What antibiotic should be used against it?

Accepted Answer

A)   Tobramycin (TOBI) 
B)  Dornase alpha (Pulmozyme) 
C)  Levalbuterol (Xopenex) 
D)  Pentamidine (NebuPent) E) A) and B)
F) All of the above

Question 3

What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis?

Accepted Answer

A)   Pulmonary edema
B)  Pleural effusion
C)  Spontaneous pneumothorax
D)  Cardiac tamponadeE) A) and B)
F) A) and C) C

Question 4

Common chest assessment findings in a patient with cystic fibrosis include:
1)  tracheal deviation.
2)  breath sounds reveal crackles and rhonchi.
3)  dull percussion note.
4)  hyperresonant percussion note.

Accepted Answer

A)  1, 3
B)  2, 4
C)  1, 2
D)  2, 3, 4E) B) and D)
F) A) and C)

Question 5

If both the mother and the father are carriers for the cystic fibrosis gene, what are the chances that their child will be a cystic fibrosis carrier?

Accepted Answer

A)   0%
B)  25%
C)  50%
D)  75%E) B) and D)
F) B) and C)

Question 6

All of the following can be used in the diagnosis of cystic fibrosis EXCEPT:

Accepted Answer

A)   an elevated potassium level in the sweat.
B)  an elevated chloride level in the sweat.
C)  genetic testing of the patient and/or parents.
D)  chronic lung infections from an early age.E) B) and C)
F) All of the above

Question 7

How can the genetic mutation found with cystic fibrosis (CF)  be characterized?
1)  There are many variations in the mutation.
2)  CF is the most common childhood inherited disorder.
3)  The mutation is a dominant trait.
4)  The mutation stops cilia function.

Accepted Answer

A)  1, 2
B)  3, 4
C)  1, 3
D)  2, 3, 4E) A) and D)
F) All of the above

Question 8

Men with cystic fibrosis have difficulty reproducing because:

Accepted Answer

A)   the fallopian tubes are blocked.
B)  the vas deferens is missing or underdeveloped.
C)  the men are impotent.
D)  the women do not ovulate.E) A) and C)
F) A) and B) B

Question 9

Which of the following is/are commonly used in the treatment of cystic fibrosis?
1)  Pancreatic enzymes and vitamins
2)  Antibiotics
3)  Postural drainage
4)  Expectorants

Accepted Answer

A)  1, 4
B)  2, 3
C)  1, 2, 3
D)  1, 2, 3, 4E) All of the above
F) A) and B)

Question 10

Which of the following are commonly cultured from the mucus in the tracheobronchial tree of a patient with cystic fibrosis?
1)  Klebsiella
2)  Pseudomonas aeruginosa
3)  Haemophilus influenzae
4)  Staphylococcus aureus

Accepted Answer

A)  1, 2
B)  2, 4
C)  1, 2, 3
D)  2, 3, 4E) B) and D)
F) B) and C)

Question 11

All of the following pulmonary function findings would be expected in a patient with moderate to severe cystic fibrosis EXCEPT:

Accepted Answer

A)   increased FVC.
B)  increased RV.
C)  decreased PEFR.
D)  decreased FEF 50%.E) All of the above
F) A) and B)

Question 12

During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have:

Accepted Answer

A)   a primarily restrictive lung disease.
B)  a primarily obstructive lung disease.
C)  equal parts restrictive and obstructive lung disease.
D)  normal airways with emphysema.E) B) and C)
F) A) and D) B

Question 13

If a cystic fibrosis patient is in generally good condition, what might be done to permanently fix the lung problem?

Accepted Answer

A)   Cryosurgery
B)  Total DNA replacement
C)  Diaphragmatic pacemaker
D)  Lung transplantE) All of the above
F) B) and D)

Question 14

Cystic fibrosis patients can have all of the following EXCEPT:

Accepted Answer

A)   malnutrition.
B)  meconium ileus (bowel obstruction) .
C)  excessive, viscous pulmonary secretions.
D)  tendency for status asthmaticus.E) None of the above
F) A) and B)

Question 15

total airway obstruction leading to atelectasis.

Accepted Answer

A)   1, 2
B)  3, 4
C)  1, 3, 4
D)  1, 2, 3, 4E) A) and B)
F) A) and C)

Exam 14: Cystic Fibrosis

Which ethnic group has the greatest number of people with cystic fibrosis?

Correct Answer
verified

Your patient has a lung infection with Pseudomonas aeruginosa. What antibiotic should be used against it?

Correct Answer
verified

What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis?

Correct Answer
verified
C

Common chest assessment findings in a patient with cystic fibrosis include: 1) tracheal deviation. 2) breath sounds reveal crackles and rhonchi. 3) dull percussion note. 4) hyperresonant percussion note.

Correct Answer
verified

If both the mother and the father are carriers for the cystic fibrosis gene, what are the chances that their child will be a cystic fibrosis carrier?

Correct Answer
verified

All of the following can be used in the diagnosis of cystic fibrosis EXCEPT:

Correct Answer
verified

How can the genetic mutation found with cystic fibrosis (CF) be characterized? 1) There are many variations in the mutation. 2) CF is the most common childhood inherited disorder. 3) The mutation is a dominant trait. 4) The mutation stops cilia function.

Correct Answer
verified

Men with cystic fibrosis have difficulty reproducing because:

Correct Answer
verified
B

Which of the following is/are commonly used in the treatment of cystic fibrosis? 1) Pancreatic enzymes and vitamins 2) Antibiotics 3) Postural drainage 4) Expectorants

Correct Answer
verified

Which of the following are commonly cultured from the mucus in the tracheobronchial tree of a patient with cystic fibrosis? 1) Klebsiella 2) Pseudomonas aeruginosa 3) Haemophilus influenzae 4) Staphylococcus aureus

Correct Answer
verified

All of the following pulmonary function findings would be expected in a patient with moderate to severe cystic fibrosis EXCEPT:

Correct Answer
verified

During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have:

Correct Answer
verified
B

If a cystic fibrosis patient is in generally good condition, what might be done to permanently fix the lung problem?

Correct Answer
verified

Cystic fibrosis patients can have all of the following EXCEPT:

Correct Answer
verified

total airway obstruction leading to atelectasis.

Correct Answer
verified

Exam 14: Cystic Fibrosis

Which ethnic group has the greatest number of people with cystic fibrosis?

Correct AnswerverifiedShow Answer

Your patient has a lung infection with Pseudomonas aeruginosa. What antibiotic should be used against it?

Correct AnswerverifiedShow Answer

What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis?

Correct AnswerverifiedC

Common chest assessment findings in a patient with cystic fibrosis include: 1) tracheal deviation. 2) breath sounds reveal crackles and rhonchi. 3) dull percussion note. 4) hyperresonant percussion note.

Correct AnswerverifiedShow Answer

If both the mother and the father are carriers for the cystic fibrosis gene, what are the chances that their child will be a cystic fibrosis carrier?

Correct AnswerverifiedShow Answer

All of the following can be used in the diagnosis of cystic fibrosis EXCEPT:

Correct AnswerverifiedShow Answer

How can the genetic mutation found with cystic fibrosis (CF) be characterized? 1) There are many variations in the mutation. 2) CF is the most common childhood inherited disorder. 3) The mutation is a dominant trait. 4) The mutation stops cilia function.

Correct AnswerverifiedShow Answer

Men with cystic fibrosis have difficulty reproducing because:

Correct AnswerverifiedB

Which of the following is/are commonly used in the treatment of cystic fibrosis? 1) Pancreatic enzymes and vitamins 2) Antibiotics 3) Postural drainage 4) Expectorants

Correct AnswerverifiedShow Answer

Which of the following are commonly cultured from the mucus in the tracheobronchial tree of a patient with cystic fibrosis? 1) Klebsiella 2) Pseudomonas aeruginosa 3) Haemophilus influenzae 4) Staphylococcus aureus

Correct AnswerverifiedShow Answer

All of the following pulmonary function findings would be expected in a patient with moderate to severe cystic fibrosis EXCEPT:

Correct AnswerverifiedShow Answer

During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have:

Correct AnswerverifiedB

If a cystic fibrosis patient is in generally good condition, what might be done to permanently fix the lung problem?

Correct AnswerverifiedShow Answer

Cystic fibrosis patients can have all of the following EXCEPT:

Correct AnswerverifiedShow Answer

total airway obstruction leading to atelectasis.

Correct AnswerverifiedShow Answer

Correct Answer
verified

Correct Answer
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C

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B

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B

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Correct Answer
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