Question 1

What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis?

Accepted Answer

A)   Pulmonary edema
B)   Pleural effusion
C)   Spontaneous pneumothorax
D)   Cardiac tamponadeE) None of the above
F) All of the above C

Question 2

All of the following pulmonary function findings would be expected in a patient with moderate to severe cystic fibrosis EXCEPT:

Accepted Answer

A)   increased FVC.
B)   increased RV.
C)   decreased PEFR.
D)   decreased FEF50%.E) A) and B)
F) C) and D)

Question 3

Which of the following are commonly cultured from the mucus in the tracheobronchial tree of a patient with cystic fibrosis?
1)  Klebsiella
2)  Pseudomonas aeruginosa
3)  Haemophilus influenzae
4)  Staphylococcus aureus

Accepted Answer

A)   1, 2
B)   2, 4
C)   1, 2, 3
D)   2, 3, 4E) A) and B)
F) A) and C)

Question 4

All of the following can be used in the diagnosis of cystic fibrosis EXCEPT:

Accepted Answer

A)   an elevated potassium level in the sweat.
B)   an elevated chloride level in the sweat.
C)   genetic testing of the patient and/or parents.
D)   chronic lung infections from an early age.E) A) and D)
F) A) and C) A

Question 5

Men with cystic fibrosis have difficulty reproducing because the:

Accepted Answer

A)   fallopian tubes are blocked.
B)   vas deferens is missing or underdeveloped.
C)   men are impotent.
D)   women do not ovulate.E) All of the above
F) B) and C)

Question 6

If both the mother and the father are carriers for the cystic fibrosis gene, what are the chances that their child will be a cystic fibrosis carrier?

Accepted Answer

A)   0%
B)   25%
C)   50%
D)   75%E) B) and C)
F) A) and B)

Question 7

Which of the following is NOT recommended in children with cystic fibrosis?

Accepted Answer

A)   Systemic corticosteroids
B)   High-dose ibuprofen
C)   Inhaled antibiotics
D)   Inhaled DNase (Dornase alpha)  (Pulmozyme) E) A) and B)
F) None of the above A

Question 8

A patient has a lung infection with Pseudomonas aeruginosa. What antibiotic should be used against it?

Accepted Answer

A)   Tobramycin (TOBI) 
B)   Dornase alpha (Pulmozyme) 
C)   Levalbuterol (Xopenex) 
D)   Pentamidine (NebuPent) E) C) and D)
F) B) and C)

Question 9

Which ethnic group has the greatest number of people with cystic fibrosis?

Accepted Answer

A)   African-Americans
B)   Asians
C)   Hispanics
D)   CaucasiansE) B) and D)
F) C) and D)

Question 10

Common chest assessment findings in a patient with cystic fibrosis include:
1)  tracheal deviation.
2)  breath sounds reveal crackles and rhonchi.
3)  dull percussion note.
4)  hyperresonant percussion note.

Accepted Answer

A)   1, 3
B)   2, 4
C)   1, 2
D)   2, 3, 4E) A) and D)
F) A) and B)

Question 11

During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have:

Accepted Answer

A)   a primarily restrictive lung disease.
B)   a primarily obstructive lung disease.
C)   equal parts restrictive and obstructive lung disease.
D)   normal airways with emphysema.E) A) and D)
F) C) and D)

Question 12

All of the following chest assessment findings may be seen in a patient with cystic fibrosis EXCEPT:

Accepted Answer

A)   decreased tactile and vocal fremitus.
B)   dull percussion note.
C)   diminished breath sounds.
D)   decreased heart sounds.E) A) and B)
F) A) and C)

Question 13

A cystic fibrosis patient in generally good condition may be a candidate for which of the following?

Accepted Answer

A)   Cryosurgery
B)   Total DNA replacement
C)   Diaphragmatic pacemaker
D)   Lung transplantE) C) and D)
F) A) and D)

Question 14

The major pathologic or structural changes associated with cystic fibrosis include:
1)  partial airway obstruction leading to hyperinflation.
2)  bronchospasm.
3)  thick, tenacious mucus.
4)  total airway obstruction leading to atelectasis.

Accepted Answer

A)   1, 2
B)   3, 4
C)   1, 3, 4
D)   1, 2, 3, 4E) A) and B)
F) B) and D)

Question 15

Which of the following may be recommended to reduce bronchial inflammation in a 12-year-old child with cystic fibrosis?

Accepted Answer

A)   High-dose ibuprofen
B)   High-dose acetaminophen
C)   High-dose naproxen
D)   High-dose corticosteroidsE) None of the above
F) A) and B)

Question 16

How can the genetic mutation found with cystic fibrosis (CF)  be characterized?
1)  There are many variations in the mutation.
2)  CF is the most common fatal childhood inherited disorder.
3)  The mutation is a dominant trait.
4)  The mutation stops ciliary function.

Accepted Answer

A)   1, 2
B)   3, 4
C)   1, 3
D)   2, 3, 4E) A) and B)
F) A) and D)

Question 17

A common nonrespiratory clinical manifestation of cystic fibrosis is:

Accepted Answer

A)   sinusitis.
B)   hyperpigmentation.
C)   rheumatoid arthritis.
D)   glaucoma.E) A) and C)
F) All of the above

Question 18

Which of the following are commonly used in the management of cystic fibrosis?
1)  Pancreatic enzymes and vitamins
2)  Antibiotics
3)  Postural drainage
4)  Expectorants

Accepted Answer

A)   1, 4
B)   2, 3
C)   1, 2, 3
D)   1, 2, 3, 4E) C) and D)
F) None of the above

Question 19

Cystic fibrosis patients can have all of the following EXCEPT:

Accepted Answer

A)   malnutrition.
B)   meconium ileus (bowel obstruction) .
C)   excessive, viscous pulmonary secretions.
D)   tendency for status asthmaticus.E) A) and B)
F) A) and C)

Exam 15: Cystic Fibrosis

What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis?

Correct Answer
verified
C

All of the following pulmonary function findings would be expected in a patient with moderate to severe cystic fibrosis EXCEPT:

Correct Answer
verified

Which of the following are commonly cultured from the mucus in the tracheobronchial tree of a patient with cystic fibrosis? 1) Klebsiella 2) Pseudomonas aeruginosa 3) Haemophilus influenzae 4) Staphylococcus aureus

Correct Answer
verified

All of the following can be used in the diagnosis of cystic fibrosis EXCEPT:

Correct Answer
verified
A

Men with cystic fibrosis have difficulty reproducing because the:

Correct Answer
verified

If both the mother and the father are carriers for the cystic fibrosis gene, what are the chances that their child will be a cystic fibrosis carrier?

Correct Answer
verified

Which of the following is NOT recommended in children with cystic fibrosis?

Correct Answer
verified
A

A patient has a lung infection with Pseudomonas aeruginosa. What antibiotic should be used against it?

Correct Answer
verified

Which ethnic group has the greatest number of people with cystic fibrosis?

Correct Answer
verified

Common chest assessment findings in a patient with cystic fibrosis include: 1) tracheal deviation. 2) breath sounds reveal crackles and rhonchi. 3) dull percussion note. 4) hyperresonant percussion note.

Correct Answer
verified

During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have:

Correct Answer
verified

All of the following chest assessment findings may be seen in a patient with cystic fibrosis EXCEPT:

Correct Answer
verified

A cystic fibrosis patient in generally good condition may be a candidate for which of the following?

Correct Answer
verified

The major pathologic or structural changes associated with cystic fibrosis include: 1) partial airway obstruction leading to hyperinflation. 2) bronchospasm. 3) thick, tenacious mucus. 4) total airway obstruction leading to atelectasis.

Correct Answer
verified

Which of the following may be recommended to reduce bronchial inflammation in a 12-year-old child with cystic fibrosis?

Correct Answer
verified

How can the genetic mutation found with cystic fibrosis (CF) be characterized? 1) There are many variations in the mutation. 2) CF is the most common fatal childhood inherited disorder. 3) The mutation is a dominant trait. 4) The mutation stops ciliary function.

Correct Answer
verified

A common nonrespiratory clinical manifestation of cystic fibrosis is:

Correct Answer
verified

Which of the following are commonly used in the management of cystic fibrosis? 1) Pancreatic enzymes and vitamins 2) Antibiotics 3) Postural drainage 4) Expectorants

Correct Answer
verified

Cystic fibrosis patients can have all of the following EXCEPT:

Correct Answer
verified

Exam 15: Cystic Fibrosis

What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis?

Correct AnswerverifiedC

All of the following pulmonary function findings would be expected in a patient with moderate to severe cystic fibrosis EXCEPT:

Correct AnswerverifiedShow Answer

Which of the following are commonly cultured from the mucus in the tracheobronchial tree of a patient with cystic fibrosis? 1) Klebsiella 2) Pseudomonas aeruginosa 3) Haemophilus influenzae 4) Staphylococcus aureus

Correct AnswerverifiedShow Answer

All of the following can be used in the diagnosis of cystic fibrosis EXCEPT:

Correct AnswerverifiedA

Men with cystic fibrosis have difficulty reproducing because the:

Correct AnswerverifiedShow Answer

If both the mother and the father are carriers for the cystic fibrosis gene, what are the chances that their child will be a cystic fibrosis carrier?

Correct AnswerverifiedShow Answer

Which of the following is NOT recommended in children with cystic fibrosis?

Correct AnswerverifiedA

A patient has a lung infection with Pseudomonas aeruginosa. What antibiotic should be used against it?

Correct AnswerverifiedShow Answer

Which ethnic group has the greatest number of people with cystic fibrosis?

Correct AnswerverifiedShow Answer

Common chest assessment findings in a patient with cystic fibrosis include: 1) tracheal deviation. 2) breath sounds reveal crackles and rhonchi. 3) dull percussion note. 4) hyperresonant percussion note.

Correct AnswerverifiedShow Answer

During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have:

Correct AnswerverifiedShow Answer

All of the following chest assessment findings may be seen in a patient with cystic fibrosis EXCEPT:

Correct AnswerverifiedShow Answer

A cystic fibrosis patient in generally good condition may be a candidate for which of the following?

Correct AnswerverifiedShow Answer

The major pathologic or structural changes associated with cystic fibrosis include: 1) partial airway obstruction leading to hyperinflation. 2) bronchospasm. 3) thick, tenacious mucus. 4) total airway obstruction leading to atelectasis.

Correct AnswerverifiedShow Answer

Which of the following may be recommended to reduce bronchial inflammation in a 12-year-old child with cystic fibrosis?

Correct AnswerverifiedShow Answer

How can the genetic mutation found with cystic fibrosis (CF) be characterized? 1) There are many variations in the mutation. 2) CF is the most common fatal childhood inherited disorder. 3) The mutation is a dominant trait. 4) The mutation stops ciliary function.

Correct AnswerverifiedShow Answer

A common nonrespiratory clinical manifestation of cystic fibrosis is:

Correct AnswerverifiedShow Answer

Which of the following are commonly used in the management of cystic fibrosis? 1) Pancreatic enzymes and vitamins 2) Antibiotics 3) Postural drainage 4) Expectorants

Correct AnswerverifiedShow Answer

Cystic fibrosis patients can have all of the following EXCEPT:

Correct AnswerverifiedShow Answer

Correct Answer
verified
C

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified
A

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified
A

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified

Correct Answer
verified